Dr. med. Dirk Manski



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Potter Syndrome: Bilateral Renal Agenesis

Definition of Potter's Syndrome

Bilateral renal agenesis (Potter's syndrome) is a rare and always fatal malformation with bilateral absent kidneys (Potter, 1965).

Epidemiology of Potter's syndrome:

Etiology of Potter's Syndrome:

Recessive inheritance is likely, siblings of children with bilateral renal agenesis are also affected in 3.5%. The absence of a ureteric bud or the absence of metanephric blastema results in the complete absence of renal tissue.

The oligohydramnios and/or the lack proline production of the kidneys leads to pulmonary hypoplasia, respiratory insufficiency and Potter facies of the children.

Signs and Symptoms of Potter's syndrome

Diagnosis of Potter's Syndrome







Index: 1–9 A B C D E F G H I J K L M N O P Q R S T U V W X Y Z



References

Potter 1965 POTTER, E. L.:
Bilateral Absence of Ureters and Kidneys: A Report of 50 Cases.
In: Obstet Gynecol
25 (1965), S. 3–12


  Deutsche Version: Bilaterale Nierenagenesie